Osteo-Hydatidosis, a zoonotic disease caused by the larval stage of the Echinococcus granulosus tapeworm, presents a significant global public health concern due to its potential morbidity and mortality. The slow growth of the parasite in the spine leads to symptoms primarily caused by spinal cord compression. It is more common in endemic areas and can cause significant mortality and morbidity. It is difficult to diagnose and treat osteohydatidosis effectively because no specific diagnostic methods are available. In most cases, surgical intervention is required to remove the cyst, decompress the spinal cord, and stabilize the affected area. This study aimed to provide insights into the clinical characteristics, diagnostic methods, laboratory findings, treatment options, and patient outcomes associated with this condition. Additionally, the study emphasized the challenges in diagnosing and treating osteohydatid disease because of the lack of specific diagnostic tools. A diagnosis of osteohydatid disease is possible in areas where it is endemic, and early diagnosis and treatment are crucial. This review summarises the current state of osteo-hydatidosis diagnosis and treatment. The healthcare sector is better positioned to face the complexity of this disease as a result of its embrace of cutting-edge technologies and multidisciplinary approaches, which will ultimately lead to improved patient treatment and pave the way for a more complete control and management strategy.